Perioperative Management of Patient with Systemic Mastocytosis Going for Total Thyroidectomy

Authors

  • Ammar AlShaker Anesthesia Department, Perioperative Medicine, Security Forces Hospital, Riyadh, Kingdom of Saudi Arabia.
  • Saud Al-Rasheedi General Surgery Department, Breast and Endocrine, Security Forces Hospital, Riyadh, Kingdom of Saudi Arabia.
  • Yousef Al-Jebrin Anesthesia Department, Security Forces Hospital, Riyadh, Kingdom of Saudi Arabia.
  • Munira Al-Masaad Anesthesia Department, Security Forces Hospital, Riyadh, Kingdom of Saudi Arabia.
  • Nawaf M. Al-Mutairi Anesthesia Department, Pain Management, Security Forces Hospital, Riyadh, Kingdom of Saudi Arabia.

DOI:

https://doi.org/10.52609/jmlph.v5i2.183

Keywords:

Anaphylaxis, Perioperative Management, Systemic Mastocytosis.

Abstract

Systemic mastocytosis (SM) is a rare disorder affecting 1 in 10,000 individuals, characterised by abnormal mast cell proliferation in extra-cutaneous organs, resulting in a variety of presentations ranging from mild asymptomatic disease to life-threatening tissue-destructive disease. Severe anaphylaxis caused by the release of histamine from mast cells can lead to poor postoperative outcomes, especially during general anaesthesia, as the severe manifestations of anaphylaxis, such as cardiovascular collapse and bronchospasm, may potentially be the first symptoms to present. In this case report, we describe the perioperative and intraoperative management of a 70-year-old female with SM, undergoing total thyroidectomy.

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Published

2025-01-18

How to Cite

AlShaker, A., Al-Rasheedi, S. ., Al-Jebrin, Y. ., Al-Masaad, M. ., & M. Al-Mutairi, N. (2025). Perioperative Management of Patient with Systemic Mastocytosis Going for Total Thyroidectomy . The Journal of Medicine, Law & Public Health, 5(2), 573–577. https://doi.org/10.52609/jmlph.v5i2.183

Issue

Vol. 5 No. 2 (2025): Apr–Jun

Section

Case Report

License

Copyright (c) 2025 Ammar AlShaker, Saud Al-Rasheedi, Yousef Al-Jebrin, Munira Al-Masaad, Nawaf M. Al-Mutairi

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